Disease Information

GTO ID(s) GTC3880
Disease NamePrimary Biliary Cholangitis
Synonymsprimary biliary cirrhosis, biliary liver cirrhosis, biliary cirrhosis, chronic nonsuppurative destructive cholangitis, primary biliary cholangitis, primary biliary cholangitis 1, biliary cirrhosis, primary, cirrhosis, biliary, liver cirrhosis, biliary, secondary biliary cholangitis, biliary cirrhosis, primary, 1, chronic non-suppurative destructive cholangitis, primary bilary cirrhosis (pbc), pbc
DefinitionDO:A liver cirrhosis characterized by chronic and slow progressive destruction of intrahepatic bile ducts.
Xref DO:12236 | EFO:0004267 | EFO:1001486 | HPO:HP:0002613 | ICD10:K74.3 | MONDO:0005388 | MONDO:0007193 | MSH:D008105 | NCI:C27167 | OMIM:109720 | ORDO:186
Disease GroupAutoimmune Disease

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