GTO ID(s) | GTC3880 |
Disease Name | Primary Biliary Cholangitis |
Synonyms | primary biliary cirrhosis, biliary liver cirrhosis, biliary cirrhosis, chronic nonsuppurative destructive cholangitis, primary biliary cholangitis, primary biliary cholangitis 1, biliary cirrhosis, primary, cirrhosis, biliary, liver cirrhosis, biliary, secondary biliary cholangitis, biliary cirrhosis, primary, 1, chronic non-suppurative destructive cholangitis, primary bilary cirrhosis (pbc), pbc |
Definition | DO:A liver cirrhosis characterized by chronic and slow progressive destruction of intrahepatic bile ducts. |
Xref | DO:12236 | EFO:0004267 | EFO:1001486 | HPO:HP:0002613 | ICD10:K74.3 | MONDO:0005388 | MONDO:0007193 | MSH:D008105 | NCI:C27167 | OMIM:109720 | ORDO:186 |
Disease Group | Autoimmune Disease |