Basic Information

Gene symbol OTC Synonyms OCTD, OTC1, OTCD, OTCase Type of gene protein-coding
Description ornithine transcarbamylase

GTO ID GTC3758
Trial ID NCT06255782
Disease Ornithine Transcarbamylase Deficiency Disease | Inborn Urea Cycle Disorder
Altered gene OTC
Therapeutic/Target gene Target gene
TherapyGene editing
Treatment ECUR-506
PhasePhase1|Phase2
Recruitment statusRecruiting
TitleA Phase I/II First-in-Human, Open-Label, Dose-Escalation Study to Evaluate the Safety and Efficacy of a Single Intravenous (IV) Administration of ECUR-506 in Males Less Than 9 Months of Age With Genetically Confirmed Neonatal Onset Ornithine Transcarbamylase (OTC) Deficiency
Year2024
CountryUnited States
Company sponsoriECURE, Inc.
Other ID(s)ECUR-506-OTC-101|OTC HOPE
Vector information
Vectoradeno-associated virus
ConstructAAV-ARCUS-OTC
Vector typeadeno-associated virus (AAV) vector
Transgene/Inserted genean ARCUS nuclease; an OTC gene

Clinical Result

Cohort 1
Administration route intravenous infusion
Pts 13
Age Child
References : iECURE Receives FDA Fast Track Designation for ECUR-506 for the Treatment of Neonatal Onset Ornithine Transcarbamylase (OTC) Deficiency

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